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Shy-Drager syndrome - Wikipedia, the free encyclopedia

Shy-Drager syndrome

From Wikipedia, the free encyclopedia

Shy-Drager syndrome is a rare, progressively degenerative disease of the autonomic nervous system. It is named after Dr Milton Shy and Dr Glenn Drager, who identified this syndrome in 1960.

It was officially deprecated as a disease entity in 1996, and existing cases were redefined as multiple system atrophy with autonomic phenomena. The name "Shy-Drager syndrome" is still used occasionally for multiple system atrophy when the primary symptoms are autonomic failure.

[edit] Notable sufferers of Shy-Drager syndome

[edit] References

  • Shy GM, Drager GA. A neurological syndrome associated with orthostatic hypotension: a clinical-pathologic study. Arch Neurol 1960;2:511-27. PMID 14446364.
  • The Consensus Committee of the American Autonomic Society and the American Academy of Neurology. Consensus statement on the definition of orthostatic hypotension, pure autonomic failure, and multiple system atrophy. Neurology 1996;46:1470. PMID 8628505.
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