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AMP deaminase - Wikipedia, the free encyclopedia

AMP deaminase

From Wikipedia, the free encyclopedia

adenosine monophosphate deaminase 1 (isoform M)
Identifiers
Symbol AMPD1
HUGO 468
Entrez 270
OMIM 102770
RefSeq NM_000036
UniProt P23109
Other data
EC number 3.5.4.6
Locus Chr. 1 p13

Myoadenylate deaminase, also called AMP deaminase, is an enzyme that converts adenosine monophosphate (AMP) to inosine monophosphate (IMP), freeing an ammonia molecule in the process. It is a part of the metabolic process that converts sugar, fat, and protein into cellular energy. In order to use energy, a cell converts one of the above fuels into adenosine triphosphate (ATP) via the mitochondria. Cellular processes, especially muscles, then convert the ATP into adenosine diphosphate (ADP), freeing the energy to do work.

A deficiency is associated with myoadenylate deaminase deficiency.

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